herediter sferositoz. English-Turkish dictionary. 3 hereditary spherocytosis. болезнь Минковского-Шоффара, гемолитическая микросфероцитарная анемия. Doctors, medical centers and hospitals experts on Herediter Sferositoz that you can contact, take appointment or send examination results. Definition of herediter sferositoz from/to (in all languages) at free online dictionary translates words and expressions between English, French, German, Italian.
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English Turkish English Login. YearVolume 44, Issue 11, Pages 27 – 34 Abstract en tr Hereditary spherocytosis HS is a relatively common hemolytic anemia; most affected individuals have mild or only moderate haemolysis It is a heterogeneous group of disorders with regard to clinical severity protein defects and mode of inheritance There is usually a family history and a typical clinical and laboratory picture so that the diagnosis is often easily made without additional laboratory tests Atypical cases may require measurement of erythrocyte membrane proteins to clarify the nature of the membrane disorder and in the absence of a family history Mild HS can be managed without folate supplementation and does not require splenectomy Moderately or severely affected individuals are likely to benefit from splenectomy which should be performed after the age of 5 6 years Turk Arch Ped ; 44 Suppl: Anemia diagnosis hereditary spherocytosis treatment.
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Am J Surg ; Haematological consequences of parvovirus B19 infec- tion. B 19 parvovirus infection causing aplastic crisis in 3 out of 5 family members with hereditary sphe- rocytosis. Ir J Med Sci Parvovirus B19 in human disease. Annu Rev Med ; Megaloblastic anemia and disor- ders of cobalamin and folate metabolism.
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Herediter Sferositoz – Global Health Guide
Rev Med Brux ; Update of guidelines for the pre- vention and treatment of infection in patients with an absent or dysfunctional spleen. Journal of the Royal College of Physicians of London ; 2: Red cell life span hegediter splenectomy in hereditary spherocytosis. J Clin Inves ; Partial splenectomy for hereditary spherocytosis.
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